Congenital high airway obstruction or stenosis is a rare malformations. The occlusion site is generally situated at the level of the larynx, with occlusion being caused by laryngeal atresia, severe subglottic stenosis, or laryngeal webs. The probable rate of approximately 50 per cent of all cases may include central nervous system anomalies, renal anomalies, and oesophageal atresia or fistula. One case were reported that Congenital high airway obstruction syndrome (CHAOS) caused by laryngeal atresia was diagnosed by prenatal ultrasound and Magnetic resonance imaging (MRI) in a male fetus at 20-weeks-gestation. Prenatal diagnosis of upper airway obstruction has been shown enlarged echogenic lungs, inverted diaphragm, fetal ascites and hydrops. fetus of airway obstruction that when breath function establish was failed or untreated for emergency tracheostomy leads to death within minutes of birth. Prenatal diagnosis of upper airway obstruction is necessary.